V2EX plakophilin

Plakophilin

释义 Definition

Plakophilin(桥粒斑蛋白):一类位于桥粒(desmosome)中的结构/连接蛋白,参与细胞与细胞之间的黏附,并与细胞骨架(尤其是中间丝)相关联;在上皮组织的稳定性与信号调控中很重要。常见成员如 plakophilin-1/2/3(PKP1/PKP2/PKP3)。在医学与病理学中也常用于讨论某些肿瘤标志物或遗传性心肌病相关基因(如 PKP2)。

发音 Pronunciation (IPA)

/plkfln/

例句 Examples

Plakophilin helps cells stick together in the skin.
桥粒斑蛋白帮助皮肤细胞彼此黏附在一起。

Loss of plakophilin can weaken desmosomes and contribute to tissue fragility.
桥粒斑蛋白的缺失会削弱桥粒结构,从而导致组织更脆弱。

词源 Etymology

来自新拉丁式科学构词:plako- 源自希腊语 plax / plakos(意为“板、斑块”,指桥粒的“斑/板状”结构),**-philin** 源自 philos(“喜爱、亲和”),整体含义可理解为“对(桥粒)斑板结构具有亲和性的蛋白”。

相关词 Related Words

文献与作品 Notable Works

  • Molecular Biology of the Cell(Alberts 等,细胞连接章节常讨论桥粒及相关蛋白,可能提及 plakophilin 家族)
  • Hatzfeld 相关综述论文(关于桥粒蛋白与 plakophilin 在细胞黏附/信号中的作用的经典综述之一)
  • 讨论 PKP2arrhythmogenic cardiomyopathy(致心律失常性心肌病) 的遗传学/综述论文(常在心脏病学与分子遗传学文献中出现 “plakophilin-2”)
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