V2EX iga nephropathy

IgA Nephropathy

定义 Definition

IgA肾病(又称“伯杰病 / Berger disease”):一种常见的原发性肾小球肾炎,特点是免疫球蛋白A(IgA)在肾小球系膜区沉积,引发炎症与损伤。常见表现包括反复血尿(有时在上呼吸道感染后出现)、蛋白尿,部分患者可进展为慢性肾病甚至肾衰竭。(该术语在更广义上也可指与IgA相关的肾脏病变,但最常用即上述疾病。)

发音 Pronunciation (IPA)

/a di e nfrpθi/

例句 Examples

She was diagnosed with IgA nephropathy after repeated episodes of blood in her urine.
她在反复出现尿血后被诊断为IgA肾病。

Although many patients have a slow course, IgA nephropathy can progress to chronic kidney disease, especially when proteinuria is persistent.
尽管许多患者病程进展缓慢,但IgA肾病在蛋白尿持续存在时可能发展为慢性肾病。

词源 Etymology

“IgA”是“Immunoglobulin A(免疫球蛋白A)”的缩写;“nephropathy”由“nephro-(肾)”+“-pathy(疾病)”构成,字面义为“肾脏疾病”。该病也常被称为“Berger disease(伯杰病)”,源于法国肾脏病学家Jean Berger在20世纪60年代对其病理特征的描述与命名传播。

相关词 Related Words

文学与典籍 Literary Works

  • Harrison’s Principles of Internal Medicine
  • Brenner & Rector’s The Kidney
  • Robbins & Cotran Pathologic Basis of Disease
  • Oxford Textbook of Clinical Nephrology
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